Myxopapillary Ependymoma In A 10-Year-Old Male

Résumé

Introduction: Spinal cord myxopapillary ependymoma (MPE) are a variant of ependymoma mostly occurring in the corda equina and/or conus medullaries of the spinal cord. They represent the most common tumors of the medullary conus mostly occurring in adults. Objectives: This is a case report of 10 years old male with a corda-equina tumor, presenting with bilateral lower limb weakness and bladder dysfunction.  Methods: The patient presented with progressive bilateral paraparesis and new onset enuresis with bilateral lower limb sensory dysfunction. Subsequent imaging revealed a T1WI isointensity solid component lesion in the spinal level of L1-L3. Elective laminectomy and resection of the spinal tumor done with gross total resection achieved and subsequent recovery of function was realized, patient on follow up in the neurosurgical clinic and has continued to gain full bladder control and lower limb power. Results: The patient underwent surgical resection of the tumor and the Histopathology reported a grade 2 Myxopapillary ependymoma. Conclusions: Myxopapillary ependymas in 2021 WHO classification were re-classified as grade 2 tumors, mostly occurring in the age group between 30-40 years. The location is the corda equina and/or conus medullaries. Treatment includes local control and it is the most important prognostic factor. Radiotherapy should be considered for all children with a localized ependymoma after surgical resection