@article{Mwangi_Nyaoncha_2022, title={Chiari Zero: A Rare Case Of Chiari Zero With Syringomyelia}, volume={1}, url={https://theeajns.org/index.php/eajns/article/view/51}, abstractNote={<p><strong>Introduction:</strong><span style="font-weight: 400;"> Chiari zero, initially dubbed syringohydromyelia without hindbrain herniation is a rare subset of Chiari malformations. The clinical presentation is usually due to the syringohydromyelia. The mode of management is mostly surgeon specific. </span><strong>Case report: </strong><span style="font-weight: 400;">We presented a 41-year-old man with an 8-year history of progressive numbness. Neurological exam revealed left sided upper limb hypopselaphesia, with diminished algesthesia and temperature sensation in the left upper limb and trunk. MRI noted cervico-thoracic syringohydromyelia with tonsillar herniation. We performed foramen magnum decompression with duraplasty. His syringomyelia reduced significantly and neurological status improved in the 3 month follow up. </span><strong>Conclusion: </strong><span style="font-weight: 400;">Chiari zero is a rare entity. Foramen magnum decompression has been the gold standard surgical modality of management. Recently, the concept of ‘central or axial’ atlantoaxial instability was introduced, paving way atlanto-axial stabilization as an alternative mode of management. </span></p>}, number={Supp 2}, journal={East African Journal of Neurological Sciences}, author={Mwangi, Ken Njau and Nyaoncha, Andrew}, year={2022}, month={Dec.}, pages={15} }